Hipertensión portal no cirrótica: presentación de cuatro casos y revisión breve de la literatura
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https://doi.org/10.52784/27112330.142Palabras clave:
hipertensión portal, sistema porta, trombosis, enfermedad vascular.Resumen
La hipertensión portal es un síndrome hemodinámico de la circulación venosa portal que condiciona múltiples complicaciones potencialmente mortales, debido a las alteraciones generadas en la circulación esplácnica y sistémica. En las últimas décadas se ha identificado la presencia de hipertensión portal en ausencia de cirrosis con un fenómeno de vasculopatía característico. Esta entidad puede clasificarse como prehepática, hepática y posthepática, según la localización del compromiso, identificado mediante estudios hemodinámicos. Se presentan cuatro casos de pacientes con hipertensión portal no cirrótica secundaria a trombosis portal. Adicionalmente, se realiza una revisión breve de la literatura, haciendo énfasis en las dos causas más frecuentes de hipertensión portal no cirrótica; la trombosis venosa portal crónica y la enfermedad vascular porto-sinusoidal.
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